Nutrition information for individuals with propionic acidemia including guidelines, toolkits, medical formulas, supplements and medical foods.
Nutrition Information
Helpful information
PROP Nutrition Guidelines
The purpose of this guideline is to foster optimum nutrition management of individuals with Propionic Acidemia (also known as PROP, PA or PPA) and reduce the uncertainty and variability in the management of PA.
PROP Toolkit
The PROP Toolkit is an international collaborative project, including case contributions from experienced metabolic dietitians working in the US, Canada, and Mexico.
Metabolic Diet App
You can track your diet through this website application on a computer or mobile device.
GNO-METAB Listserv
Publications
Dietary practices in propionic acidemia: A European Survey
Dietary Practice in Propionic Acidemia: Parent Caregiver Perspectives and Practices.
Low protein Diet
One of the most common treatments in Propionic Acidemia is the restriction of natural protein or whole intact protein in foods and formula. The specifics of the diet are followed by a dietitian or medical provider and are monitored with growth, development and labs.
Formula supplementation
Frequently, not enough protein is taken in through diet because of protein restriction for growth and development, so formulas are used to increase the amount of protein in the diet. This is done through formulas that do not have or have very little valine, isoleucine, threonine, and methionine. The amount in the diet changes with growth, development, labs, and other factors.
There are a number of formulas that are available to drink or go through a feeding tube. In the United States, the formulas can often be obtained from a durable equipment supply company, state programs, and sometimes pharmacies.
Need help? The Formula4Success program at Vitaflo offers step-by-step, detailed information and support to get the Vitaflo™ products you need.
Some of the formulas available are:
Abbott Nutrition
Protein-free to permit protein restriction or the addition of extra energy, minerals, and vitamins.
Methionine and valine-free to allow greater intake of intact protein.
Methionine and valine-free to allow greater intake of intact protein.
Cambrooke Therapeutics
Promactin AA Plus Berry
Promactin AA Plus is a methionine, threonine, and valine–free, isoleucine low, nutritionally complete, ready-to-drink, amino acid based medical food for the dietary management of Methylmalonic Acidemia (B12 non-responsive) or Propionic Acidemia.
Promactin AA Plus has a creamy, non-acid taste profile in an all-natural Berry flavor. Suitable for ages 1 through adult.
Mead Johnson
A protein- and amino acid-free product designed with carbohydrates, vitamins and minerals as well as the essential fatty acids.
A protein- and amino acid-free product designed with carbohydrates, vitamins and minerals as well as the essential fatty acids
Nutricia
Vitaflow
low isoleucine protein substitute
free and low isoleucine protein substitute
Disclaimer
The Propionic Acidemia Foundation website is designed for educational purposes only and is not intended to serve as medical advice. The information provided on this site should not be used for diagnosing or treating a health problem or disease. It is not a substitute for professional care. If you suspect that you or your children may have Propionic Acidemia, you should consult your health care provider.
The Propionic Acidemia Foundation does not recommend nor endorse any particular products, companies, or manufacturers.